目的 探讨先天性绞扼轮综合征的手术治疗方法。方法 2013年7月—2018年11月手术治疗先天性绞扼轮综合征患儿9例,均采用一期手术切除束带,Z形松解成形的方法进行治疗,其中2例小腿束带合并马蹄内翻足患儿先予束带切除、成形手术,术后1年行在Ponseti石膏疗法基础上行马蹄内翻足软组织广泛松解、肌腱转移手术。结果 9例全部手术切口愈合良好,未出现皮瓣坏死,环状缩窄带得到充分松解。2例小腿束带合并马蹄内翻足术后畸形矫正满意,未出现复发。结论 1期手术切除束带并松解成形,不会导致皮瓣的坏死,而且可获得较满意的外观,Ponseti石膏疗法基础上行马蹄内翻足软组织广泛松解、肌腱转移手术是治疗束带合并马蹄内翻足优良的手术方法。

Objectives To introduce the surgical treatment experience of congenital constriction band syndrome. Methods From July 2013 to November 2018, nine children with congenital constriction band syndrome adopted stage-one surgical removal of the band and Z-plasty, among which two cases of lower leg band combined with talipes equinovarus additionally received extensive soft tissue release of talipes equinovarus and tendon transfer operation based on Ponseti plaster therapy one year later. Results All the surgical incisions of the nine cases healed well, no flap necrosis occurred, and the annular constricted narrow bands were fully released. The surgical effects for the two cases of lower leg band combined with talipes equinovarus were satisfactory without recurrence. Conclusion Stage-one surgical removal of the band and release of the soft tissue will not lead to necrosis of the skin flap, and can obtain a satisfactory appearance. Extensive soft tissue release and tendon transfer of talipes equinovarus based on Ponseti plaster treatment is an excellent surgical method for the treatment of constriction band combined with talipes equinovarus.