Abstract: Objective To investigate the clinical features of idiopathic pulmonary fibrosis (IPF). Methods One patient with idiopathic pulmonary fibrosis was diagnosed by integrating clinical, radiologic and pathologic information and clinical data of this case was analyzed. Results The patient described in the present case was a 70-year-old male who presented with 2 years history of progressive dyspnea. Pulmonary function testing revealed severe restrictive ventilator impairment and the diffusing capacity for carbon monoxide was reduced. The histological examination showed a pattern of usual interstitial pneumonia (UIP). Conclusions The pathological diagnosis of IPF should be identified combing clinical features and findings on lung HRCT.

Key words: Idiopathic pulmonary fibrosis, Idiopathic interstitial pneumonia, Diagnosis